Clinical Trial: The Regional Scintigraphic DPD Uptake in Cardiac Transthyretin Amyloidosis.
Study Status: Completed
Recruit Status: RECRUITING
Condition: Transthyretin Amyloidosis
Study Type: OBSERVATIONAL
Official Title: The Comparisons of Regional Scintigraphic DPD Uptake Between Patients With Hereditary and Wild Type Cardiac Transthyretin Amyloidosis
Brief Summary:
Cardiac transthyretin (ATTR) amyloidosis is an infiltrative cardiomyopathy with an inexorably progressive clinical course and poor prognosis.The disease is caused by misfolding of the liver-derived precursor protein transthyretin as a result of an acquired wild-type variant (ATTRwt) or as a hereditary mutant variant (ATTRm).Application of single-photon emission computed tomography (SPECT) provides greater anatomic resolution, enabling the assessment of amyloid burden within individual left ventricle segments.This…
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